Control examination were made in tampere university hospital and in the paediatric cardiologic unit of helsinki university hospital. Taussigbing syndrome is a cyanotic congenital heart defect in which the patient has both double outlet right ventricle dorv and subpulmonic ventricular septal defect vsd in dorv, instead of the normal situation where blood from the left ventricle lv flows out to the aorta and blood from the right ventricle rv flows out to the pulmonary artery, both aorta and pulmonary artery are. Primary arterial switch operation as a strategy for total. Methods and results a retrospective study was performed, and 43 patients with taussigbing anomaly were identified between 1990 and 2011. Arterial switch versus kawashima intraventricular repair. Blalocktaussig shunt, also known as blalockthomastaussig shunt, is a palliative procedure designed to increase pulmonary arterial blood flow in patients with right ventricular outflow tract obstruction e. Taussigbing anomaly and coarctation of the aorta in infancy. There are 0 terms under the parent term taussig bing syndrome in the icd10cm alphabetical index. We describe the outcomes after aso in patients with tba at a single institution. Taussigbing anomaly is a rare congenital heart malformation and is one of the variants of double outlet right ventricle it consists of transposition of the aorta to the right ventricle and malposition of the pulmonary artery with subpulmonary ventricular septal defect history and etymology. The clinical manifestations of a taussig bing anomaly, therefore, are much like those of dextrotransposition of the great arteries but the surgical repair is different. Quantitative anatomy of taussig bing anomaly leo a bockeria 1, osman a makhachev 1,2, margarita v gorgeeva 1, marina s panova 1, t atiana y u philippkina 1, titalav kh khiriev 1 and sergey b. Between 1983 and 1994, 20 children under went intracardiac repair of taussig bing anomaly. Operative mortality in the current era is between 0% and 7%.
Longterm results article pdf available in european journal of cardiothoracic surgery. Median age at arterial switch operation was 7 range, 2192 days, and median operative weight was 3. Singlestage neonatal repair of taussigbing anomaly. Jul 27, 2017 taussigbing anomaly and aortic arch obstruction are two types of complex congenital cardiac malformations.
Singlestage correction for taussigbing anomaly associated. Taussig bing syndrome the icd10cm alphabetical index is designed to allow medical coders to look up various medical terms and connect them with the appropriate icd codes. Taussigbing anomaly is defined as an anomalous ventriculoarterial connection with vsd and dorv. In addition, tricuspidaorta discontinuities are present. Taussig bing anomaly named after the authors that first described it helen b. Quantitative anatomy of taussigbing anomaly leo a bockeria 1, osman a makhachev 1,2, margarita v gorgeeva 1, marina s panova 1, t atiana y u philippkina 1, titalav kh khiriev 1 and sergey b. Taussigbing anomaly is a rare congenital heart malformation that was first described in 1949 by helen b. Patients with taussigbing anomaly and aorticarch obstruction may have a higher reoperation rate than those with normalarch anatomy. Taussigbing anomaly was first described by taussig and bing in 1949. The taussigbing anomaly is relatively rare and it accounted for approximately 8% of cases in sridaromont series.
In 1950, the similar case was reported, and the anomaly was eventually named the taussigbing heart 2. Experience from a tertiary care center in the developing world. Full text pdf 1711k abstracts references28 from 1985 through 1994, 12 consecutive patients with taussigbing anomaly underwent an arterial switch. To assess the longterm results of the arterial switch operation aso for taussigbing anomaly. Taussigbing anomaly is a rare congenital cardiac malformation that was first described in 1949 by taussig 18981986 and bing konstantinov, 2009. Despite surgical complexity, results of the arterial switch operation for taussigbing anomaly are good. The arterial switch operation with vsd closure can be applied without ventriculotomy to all great artery relationships and allows neonatal repair with or. Echocardiographic case report of overriding and straddling of the mitral valve in taussigbing anomaly. In 1950, the similar case was reported, and the anomaly was eventually named the taussig bing heart 2. To assess the longterm results of the arterial switch operation aso for taussig bing anomaly.
Spontaneous vaginal delivery happened at the 41 week without problems. Blalock taussig shunt, also known as blalockthomas taussig shunt, is a palliative procedure designed to increase pulmonary arterial blood flow in patients with right ventricular outflow tract obstruction e. Pulmonary root translocation for repair of taussigbing. Apr 29, 2015 symptoms, risk factors and treatments of taussigbing syndrome medical condition taussigabing syndrome is a cyanotic congenital heart defect in which the patient has both double outlet. Although substantial improvement has since been achieved in surgical results of the repair of the anomaly, management of the taussigbing anomaly remains challenging. Taussigbing disease definition of taussigbing disease. The great arteries had a sidebyside relationship and a large size discrepancy. Taussig bing is a form of double outlet right ventricle that is characterized by the presence of subpulmonary ventricular septal defect, double conus and side by side great arteries. Echocardiographic case report of overriding and straddling of the mitral valve in taussig bing anomaly. Taussigbing anomaly and aortic arch obstruction are two types of complex congenital cardiac malformations.
Among four, one patient had taussig bing anomaly and coarctation of aorta with 1 left circumflex and 2 right sided coronary artery, another had intramural origin of right coronary artery and left coronary artery, both of which were arising from left facing sinus. The icd10cm alphabetical index is designed to allow medical coders to look up various medical terms and connect them with the appropriate icd codes. The coexistence of the taussigbing anomaly and coarctation of the aorta is a highly complex situation carrying a dismal prognosis. Read more about symptoms, diagnosis, treatment, complications. Taussig bing anomaly, transposition of the great arteries, arterial switch operation, left ventricular outflow tract obstruction, right ventricular outflow tract obstruction introduction the taussig bing heart tbh represents a complex subset of double outlet right ventricle. Taussigbing syndrome definition of taussigbing syndrome. Despite surgical complexity, results of the arterial switch operation for taussig bing anomaly are good. Arterial switch for transposition of the great arteries with large ventricular septal defect and for taussig bing anomaly. Bing is a cyanotic congenital heart disease characterized by the dual presence of a subpulmonic ventricular septal defect vsd along with a double outlet right ventricle dorv. Although this cardiac malformation was first described 60 years ago, 1 its management still presents a. Comas and carmelo mignosa and andrew donald cochrane and james l.
Taussigbing anomaly university of medicine and dentistry. Objective aortic arch obstruction is a commonly associated problem in the taussigbing anomaly. Patwary me, khan ms, marwah a, singh v, shekhawat s, sharma r. This is similar in many ways to transposition with a vsd and it may be treated with an arterial switch operation along with a patch within the. Outcome of total correction of taussigbing anomaly. From 20 to 2015, 4 patients were presented with taussig bing anomaly. The article in this issue of the journal by vergnat and colleagues reports the largest singleinstitution experience with the surgical treatment of doubleoutlet right ventricle dorv with subpulmonary ventricular septal defect vsd, also known as the taussigbing anomaly. A heart malformation known as taussigbing anomaly also called taussigbing syndrome, heart, or malformation consists of transposition of the aorta to the right ventricle and malposition of the pulmonary artery with subpulmonary ventricular septal defect vsd fig. It can be corrected surgically also with the arterial switch operation aso.
Late outcomes after arterial switch operation for taussig bing anomaly mathieu vergnat, md,a albanelouen baruteau, md,a,b lucile houyel, md,a mohamedou ly, md,a regine roussin, md,a andre capderou, md, phd,b,c virginie lambert, md, phd,a,c and emre belli, mda objective. Between 1983 and 1995, 28 consecutive patients with taussigbing anomaly underwent arterial switch operation with baffling of the left ventricle to neoaorta. Clinical outcomes of primary arterial switch operation in. Total repair with closure of ventricular sedtal defect. The article in this issue of the journal by vergnat and colleagues reports the largest singleinstitution experience with the surgical treatment of doubleoutlet right ventricle dorv with subpulmonary ventricular septal defect vsd, also known as the taussig bing anomaly. Almost 50% of patients with taussigbing anomaly have aortic arch obstruction. Between 1983 and 1994, 20 children under went intracardiac repair of taussigbing anomaly. She is credited with developing the concept for a procedure that would extend the lives of children born with tetralogy of fallot the most common cause of blue baby syndrome. The surgery was performed with translocation of the aortic root to the left ventricular outflow tract and the pulmonary root to the right ventricular outflow tract, after closure of the ventricular septal defect with a patch that ultimately directed flow from the left ventricle. Abstract taussigbing anomaly and aortic arch obstruction are two types of complex congenital cardiac malformations. This anomaly was initially described in 1949 as transposition. Singlestage neonatal repair of taussigbing anomaly bahaaldin alsou. From 1985 through 1994, 12 consecutive patients with taussig bing anomaly underwent an arterial switch.
Between 1983 and 1994, 20 children underwent intracardiac repair of taussigbing anomaly. Type a interrupted aortic arch with taussigbing anomaly. Late outcomes after arterial switch operation for taussig. Arterial switch operation in patients with taussig bing. Taussig bing anomaly is a rare congenital heart malformation and is one of the variants of double outlet right ventricle it consists of transposition of the aorta to the right ventricle and malposition of the pulmonary artery with subpulmonary ventricular septal defect. Age at operation varied from 8 to 42 months mean 21 months. A heart malformation known as taussigbing anomaly also called taussig bing syndrome, heart, or malformation consists of transposition of the aorta to the right ventricle and malposition of the pulmonary artery with subpulmonary ventricular septal defect vsd fig. The coexistence of the taussig bing anomaly and coarctation of the aorta is a highly complex situation carrying a dismal prognosis. Taussigbing anomaly american journal of cardiology. Between november 2006 and november 2015, 39 neonates with taussigbing anomaly and aortic arch. Dec 16, 2015 from 20 to 2015, 4 patients were presented with taussig bing anomaly. Taussigbing anomaly the annals of thoracic surgery.
Coarctation of the aorta was present in 6 patients including 4 with hypoplasia of the aortic arch, interruption of the aortic arch in one, straddling mitral valve in one and. Taussigbing is a form of double outlet right ventricle that is characterized by the presence of subpulmonary ventricular septal defect, double conus and side by side great arteries. Taussig bing anomaly is defined as an anomalous ventriculoarterial connection with vsd and dorv. Coarctation of the aorta was present in 6 patients including 4 with hypoplasia of the aortic arch, interruption of the aortic arch. The characteristic feature of the taussigbing anomaly tba. Coronary pattern was a single coronary artery arising anteriorly from the right coronary sinus, too far to be transferred to the pulmonary artery. Although this cardiac malformation was first described 60 years ago, 1 its management still presents a challenge to. Surgical results of arterial switch operation for taussig. Although various alternative repair strategies have been developed through the years,25 the closure of the ventricular septal defects vsds tunneling the left ventricular outflow tract to the pulmonary valve followed by arterial switch operation was accepted as the method of choice, particularly in the. For children with taussig bing anomaly, the kawashima intraventricular repair for sidebyside great arteries preserves the native aortic valve and avoids coronary dissection. Taussig and bing emphasized that the overriding of pulmonary artery was an integral part of this malformation.
In these cases, the pulmonary stenosis 11 does not occur, the pulmonary trunk is markedly dilated as in figure 25 and there is a high vsd immediately subjacent to the pulmonary valve subpulmo. Taussigbing heart although the anomaly was presented schematically fig. Late outcomes after arterial switch operation for taussigbing anomaly mathieu vergnat, md,a albanelouen baruteau, md,a,b lucile houyel, md,a mohamedou ly, md,a regine roussin, md,a andre capderou, md, phd,b,c virginie lambert, md, phd,a,c and emre belli, mda objective. Taussigbing anomaly and coarctation of the aorta in. The arterial switch operation aso is associated with poorer outcomes in patients with taussig bing anomaly tba compared with transposition of the great arteries tga. Aortic arch obstruction is a commonly associated problem inthe taussigbing anomaly.
The double root switch was used to repair a taussigbing anomaly in a twomonthold child. The characteristic feature of the taussigbing anomaly tba that makes. Complex transposition of great arteries tga is when additional conotruncal anomalies coexist with a tga. Pdf quantitative anatomy of taussigbing anomaly researchgate. Taussig bing is one of the variants of the double outlet right ventricle. Quantitative anatomy of taussigbing anomaly leo a bockeria 1, osman a makhachev 1,2, margarita v gorgeeva 1, marina s panova 1, t atiana y. The vsd is subpulmonary in location and the outlet septum is malaligned. This report contributes significantly to the aggregate surgical experience with this. Taussigbing anomaly is a rare congenital cardiac malformation, first described in 1949 by helen b. We report a case of staged repair of type a interrupted aortic arch with taussigbing anomaly in a one month old male.
Taussigbing is one of the variants of the double outlet right ventricle. To assess the longterm results of the arterial switch operation aso for. Outcomes of the arterial switch operation in patients with. Helen brooke taussig may 24, 1898 may 20, 1986 was an american cardiologist, working in baltimore and boston, who founded the field of pediatric cardiology. The article in this issue of the journal by vergnat and colleagues reports the largest singleinstitution experience with the surgical treatment of doubleoutlet right. This report assesses the surgical outcomes of singlestage correction in neonates with both defects. Double outlet right ventricle dorv taussigbing malformation tetralogy of fallot with extreme dextroposition of the aorta eisenmengers anomaly eisenmenger ventricular septal defect european paediatric cardiac code reference of double outlet right ventricle is 01. Between 1983 and 1995, 28 consecutive patientswith taussigbing anomaly underwent arterial switch operation with bafflingof the left ventricle to neoaorta.
This anomaly was eventually named as tausbing heart in 1950 sig by lev and associates 9and subsequently introduced the spectrum of taussig bing hearts depending on. Complete transposition of the aorta and a levoposition of the pulmonary artery. Between november 2006 and november 2015, 39 neonates with. Taussingbing anomaly, with or without aortic archobstruction, can be repaired with arterial switch operation during theneonatal period with good outcome. The characteristic feature of the taussig bing anomaly tba that makes. This anomaly was initially described in 1949 as transposition of the great arteries 1. Singlestage repair of taussigbing anomaly and interrupted aortic archtype a. Current corrective surgical approaches for the taussigbing heart include arterial switch with ventricular septal defect vsd closure and intraventricular repair as described by kawashima. Quantitative anatomy of taussigbing anomaly longdom. In the type called the taussig bing anomaly top right diagram 2 blood from the lv passes through the vsd to the pulmonary artery, whilst blood from the rv tends to be directed mainly to the aorta. Taussigbing anomaly consists of transposition of the aorta to the right ventricle and malposition of the pulmonary artery with subpulmonary ventricular septal defect vsd taussig and bing. The arterial switch operation aso is associated with poorer outcomes in patients with taussigbing anomaly tba compared with transposition of the great arteries tga. Singlestage neonatal repair of taussigbing anomaly core. Notable reasons for staged repair include the need to the need to adapt the left ventricle to the systemic high pressures.
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